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mielofibroza
4. MDS/MPN
4.1. Chronic myelomonocytic leukemia (CMML)
4.2. Atypical chronic myeloid leukemia, BCR-ABL1 negative
4.3. Juvenile myelomonocytic leukemia (JMML)
4.4. MDS/MPN, unclassifiable
4.4.1. Provisional entity: refractory anemia with ring sideroblasts associated with
marked thrombocytosis (RARS-T)
70%
AML 30%
1951- BMPC:
PV, TE, MFI, LMC
Kralovi Nangal
cs et Pikman Klamp
et al, fl et al, ia et al,
al, 2013
2005 2006 2013
Gena PV TE PMF
PV
TE
MFI
MMM: evolutie
Faza de proliferare=> insuficienta medulara
1=> 15 ani
MMM : tratament
Substitutie ME
Androgeni
Interferon
Anagrelida
Thalidomida