Documenti di Didattica
Documenti di Professioni
Documenti di Cultura
Treatment evaluation in
congenital abdominal wall
defects
C. Sabetay, O Ciobanu, Anca Malos, E Carstoiu
Department of Pediatric Surgery, Emergency Hospital Craiova, Prof. Dr. Corneliu SABETAY
ETIOPATHOGENY
Chromosomal anomalies
important factor
The cariotype
not a very
normal
Department of Pediatric Surgery, Emergency Hospital Craiova, Prof. Dr. Corneliu SABETAY
Number of cases - 62
45 cases omphalocele
17 cases gastroschisis
Department of Pediatric Surgery, Emergency Hospital Craiova, Prof. Dr. Corneliu SABETAY
OMPHALOCELE
AITKENS CLASSIFICATION
1st group
abdominal wall
flaw under
8cm
28 cases (62,3%)
2nd group
abdominal
wall flaw
over 8 cm
17 cases (37,7%)
Department of Pediatric Surgery, Emergency Hospital Craiova, Prof. Dr. Corneliu SABETAY
DIFFERENTIAL
DIAGNOSIS
Umbilical hernia
Intracordonal omphalocele
(misinterpreted as umbilical
hernia)
Meckels diverticulitis
with Secondary peritonitis
Department of Pediatric Surgery, Emergency Hospital Craiova, Prof. Dr. Corneliu SABETAY
Extrophy of cloaca
Umbilical tumor
Department of Pediatric Surgery, Emergency Hospital Craiova, Prof. Dr. Corneliu SABETAY
ASSOCIATED MALFORMATIONS
(17 cases)
Common mesentery 8 cases
Persistence of the omphaloenteric canal and Meckel
diverticle 4 cases
Urinary bladder extrophy 2 cases
Heart malformations 3 cases
Omphalocele
Left radius agenesia
Coronary hypospadias
Heart malformation
Department of Pediatric Surgery, Emergency Hospital Craiova, Prof. Dr. Corneliu SABETAY
OMPHALOCELE - TREATMENT
25 cases, pure forms of omphalocele;
(Aitkens 1st group)
Surgical Gross method good results
20 cases
group
Aitkens 2nd
Schuster, Allen,
Wren, Fufezan
Department of Pediatric Surgery, Emergency Hospital Craiova, Prof. Dr. Corneliu SABETAY
Aitkens
1st group
Department of Pediatric Surgery, Emergency Hospital Craiova, Prof. Dr. Corneliu SABETAY
Grosss method
Final result
Department of Pediatric Surgery, Emergency Hospital Craiova, Prof. Dr. Corneliu SABETAY
Aitkens
2nd group
Department of Pediatric Surgery, Emergency Hospital Craiova, Prof. Dr. Corneliu SABETAY
(continued)
Department of Pediatric Surgery, Emergency Hospital Craiova, Prof. Dr. Corneliu SABETAY
Conservative
treatment
Department of Pediatric Surgery, Emergency Hospital Craiova, Prof. Dr. Corneliu SABETAY
Grobs method
intermediary
results (1)
Department of Pediatric Surgery, Emergency Hospital Craiova, Prof. Dr. Corneliu SABETAY
Grobs method
intermediary
results (2)
Department of Pediatric Surgery, Emergency Hospital Craiova, Prof. Dr. Corneliu SABETAY
Grobs method
intermediary
results (3)
Department of Pediatric Surgery, Emergency Hospital Craiova, Prof. Dr. Corneliu SABETAY
Grobs method
Final result
Department of Pediatric Surgery, Emergency Hospital Craiova, Prof. Dr. Corneliu SABETAY
Gastroschisis
-primary closure
-secondary closure
Gore-Tex
Silicon bag
Department of Pediatric Surgery, Emergency Hospital Craiova, Prof. Dr. Corneliu SABETAY
Silicon bag
Department of Pediatric Surgery, Emergency Hospital Craiova, Prof. Dr. Corneliu SABETAY
Day 5
Day 6
Department of Pediatric Surgery, Emergency Hospital Craiova, Prof. Dr. Corneliu SABETAY
Day 10
Department of Pediatric Surgery, Emergency Hospital Craiova, Prof. Dr. Corneliu SABETAY
Omphalocele
and
Gastroschisis
Embryology
Migration
defect
closure
Anatomy
Median defect,
with sac
always
Associated malformations
Yes +++
Rare +/-
Treatment/surgery
Not an emergency
Conservative treatment
Emergency, precocious
surgical treatment
Nutrition
Precocious
TPN
Good
Department of Pediatric Surgery, Emergency Hospital Craiova, Prof. Dr. Corneliu SABETAY
presentation
time
-Associated malformations
-Rupture of the membranes (sac) in
case of omphalocele
-Size of defect (omphalocele)
-Immaturity
-Respiratory complications