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doi: 10.5606/kbbihtisas.2015.82335
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ABSTRACT
Laryngeal leiomyosarcoma is an extremely rare malignancy originating from the smooth muscles of blood vessels. Herein, we present
the first case of leiomyosarcoma arising from the glottic area of the larynx with coexistent tuberculous mediastinal lymphadenopathy.
The patient was treated with vertical laryngectomy and anti-tuberculous medication. He has been disease-free for 24 months since
initial treatment.
Keywords: Larynx; leiomyosarcoma; mediastinal lymphadenopathy; vertical laryngectomy.
Z
Larengeal leiomiyosarkom, kan damarlarnn dz kaslarndan kken alan, son derece nadir bir malignitedir. Bu yazda, elik eden
tberkloz mediastinal lenfadenopati ile birliktelik gsteren larenksin glottik blgesinden kken alan ilk leiomiyosarkom olgusu sunuldu.
Hasta vertikal larenjektomi ve antitberkloz ilalar ile tedavi edildi. lk tedaviden bu yana 24 aydr hasta hastalkszdr.
Anahtar Szckler: Larenks; leiomiyosarkom; mediastinal lenfadenopati; vertikal larenjektomi.
Received / Geli tarihi: September 07, 2013 Accepted / Kabul tarihi: April 15, 2014
Available online at
www.kbbihtisas.org
doi: 10.5606/kbbihtisas.2015.82335
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CASE REPORT
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(a)
(b)
(c)
(d)
Figure 4. (a) Spindle cell neoplasm with atypia and pleomorphism underlying squamous
epithelium (H-E x 200). (b) Actin expression (IHC x 400). (c) H-Caldesmon
expression (IHC x 400). (d) Ki-67 expression (IHC x 400).
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