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Prenatal-Polyhydramnios, dilated bowel Feeding intolerance Emesis Abdominal distension Failure to pass meconium
WHAT DO I DO
PHYSICAL EXAM ABCS RESCITATION ALONG WITH EVALUATION FIGURE OUT THE PROBLEM
FURTHER EVALUATION
SERIAL ABDOMINAL XRAYS OROGASTRIC TUBE CONTRAST STUDIES
UGI TO R/O MALROTATION BE TO EVALUATE LOWER GI TRACT REMEMBER TO GIVE FLUIDS
ESOPHAGEAL ATRESIA/TEF
INCREASED SALIVATION RESP DISTRESS/CYANOSIS ABDOMINAL DISTENSION PNEUMONIA
EA/TEF-MANAGEMENT
HEAD ELEVATED AND PRONE POSITION REPLOGLE TUBE IN THE POUCH IV ACCESS IV ANTIBIOTICS AVOID INTUBATION IF POSSIBLE
EA/TEF-ASSOCIATED ANOMALIES
VATER SYNDROME
CARDIAC ECHO-EVAL SIDE OF AORTIC ARCH RENAL SONO PERINEAL EXAM
DUODENAL OBSTRUCTION
MALROTATION UNTIL PROVEN OTHERWISE PARTIAL VS COMPLETE OBSTRUCTION VOLVULUS IS A TRUE SURGICAL EMERGENCY
MECONIUM ILEUS
VOMITING/DISTENSION XRAYS-DISTAL DILITATION, SOAP BUBBLE IN LUMEN CONTRAST ENEMA-MICROCOLON WITH MECONIUM PELLETS IV/IV ANTIBIOTICS CYSTIC FIBROSIS TESTING
HIRSCHSPRUNGS DISEASE
SLOWER ONSET OF SYMPTOMS DISTENSION, DELAYED MECONIUM PASSAGE, ENTERCOLITIS XRAYS-DILATED COLON LOOPS DDX-HYPOPLASTIC LEFT COLON SYNDROME, INTESTINAL DYSPLASIA CONTRAST ENEMA RECTAL BIOPSY MANDATORY
ANORECTAL MALFORMATION
FAILURE TO PASS MECONIUM PHYSICAL EXAM MANDATORY SERIAL XRAYS ULTRASOUND HELPFUL ASSOCIATED ANOMALIES
RENAL U/S MANDATORY VATER SYNDROME
GASTROSCHISIS
DEFECT TO RIGHT OF UMBILICUS FLUID/TEMPERATURE LOSSES COVER BOWEL IN BAG/MOIST GAUZE LATERAL POSITION/SUPPORT BOWEL FREQUENT EXAMS REPLOGLE TUBE/IV ANTIBIOTICS
OMPHALOCELE
DIFFERENT THAN GASTROSCHISIS VARYING DEGREES OF HERNIATION LESS FLUID/HEAT LOSSES ASSOCIATED ANOMALIES
CARDIAC GENETIC BECKWITH-WEIDEMANN-SUGARS
Necrotizing Enterocolitis
Most common surgical ICN emergency Major risks-Prematurity, ?early feeds Minor risks-Stress, shock Most often affects small bowel Despite theories-Unclear etiology
NEC-Clinical diagnosis
Distension, lethargy, feeding intolerance Bilious emesis, bleeding KUB-Pneumatosis intestinalis, portal venous gas, pneumoperitoneum
NEC-BELL CLASSIFICATION
A-Suspected NEC
Mild distension, vomiting, mild ileus
B-Definite NEC
Marked distension, bleeding, pneumatosis, PV gas
C-Advanced NEC
Sepsis, shock, pneumoperitoneum, surgical Rx
NEC-MEDICAL MANAGEMENT
ABCs Pan-culture, begin triple antibiotics Correct coagulopathy Serial exams, X-Rays, labs Surgical input